Sulfatase Modifying Factor 1/SUMF1 Products
Mammalian sulfatases have a common CXPXR motif, in which the Cys residue is post-translationally modified to a Calpha-formylglycine (FGly) residue. This modification is essential for catalytic activity of all sulfatases and is catalyzed by FGly generating enzyme (FGE) encoded by sulfatase modifying factor 1 (SUMF1). FGE deficiency causes multiple sulfatase deficiency (MSD), a rare autosomal recessive disorder. SUMF2 does not have FGly enzymatic activity, but may compete with SUMF1 for the same substrate.
101 results for "Sulfatase Modifying Factor 1/SUMF1" in Products
101 results for "Sulfatase Modifying Factor 1/SUMF1" in Products
Sulfatase Modifying Factor 1/SUMF1 Products
Mammalian sulfatases have a common CXPXR motif, in which the Cys residue is post-translationally modified to a Calpha-formylglycine (FGly) residue. This modification is essential for catalytic activity of all sulfatases and is catalyzed by FGly generating enzyme (FGE) encoded by sulfatase modifying factor 1 (SUMF1). FGE deficiency causes multiple sulfatase deficiency (MSD), a rare autosomal recessive disorder. SUMF2 does not have FGly enzymatic activity, but may compete with SUMF1 for the same substrate.
| Reactivity: | Human, Mouse |
| Details: | Mouse IgG2B Monoclonal Clone #329005 |
| Applications: | WB, IP |
| Reactivity: | Mouse |
| Details: | Goat IgG Polyclonal |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB |
| Applications: | ELISA |
| Reactivity: | Human, Mouse |
| Details: | Goat IgG Polyclonal |
| Applications: | WB, ELISA |
| Applications: | ELISA |
| Applications: | PAGE |
| Applications: | AC |
| Applications: | PAGE |
| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC |
| Applications: | WB |
| Reactivity: | Human, Mouse |
| Details: | Mouse IgG2B Monoclonal Clone #329005 |
| Applications: | WB, IP |
| Reactivity: | Human, Mouse |
| Details: | Mouse IgG2B Monoclonal Clone #329005 |
| Applications: | WB, IP |
| Reactivity: | Mouse |
| Details: | Goat IgG Polyclonal |
| Applications: | WB |
| Reactivity: | Mouse |
| Details: | Goat IgG Polyclonal |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB |
| Reactivity: | Human, Mouse |
| Details: | Mouse IgG2b Monoclonal Clone #329005 |
| Applications: | WB, IP |
| Reactivity: | Mouse |
| Details: | Goat IgG Polyclonal |
| Applications: | WB |
| Reactivity: | Human, Mouse |
| Details: | Mouse IgG2b Monoclonal Clone #329005 |
| Applications: | WB, IP |
| Reactivity: | Human, Mouse |
| Details: | Mouse IgG2b Monoclonal Clone #329005 |
| Applications: | WB, IP |
| Reactivity: | Human, Mouse |
| Details: | Mouse IgG2b Monoclonal Clone #329005 |
| Applications: | WB, IP |
| Reactivity: | Human, Mouse |
| Details: | Mouse IgG2b Monoclonal Clone #329005 |
| Applications: | WB, IP |
| Reactivity: | Human, Mouse |
| Details: | Mouse IgG2b Monoclonal Clone #329005 |
| Applications: | WB, IP |