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238 results for "alpha-Galactosidase A/GLA" in Products

alpha-Galactosidase A/GLA Products

Galactosidase alpha encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq]

Applications: ELISA
Human alpha-Galactosidase A/GLA ELISA Kit (Colorimetric)
(2)
Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #1029705
Source: CHO
Accession #: P06280
Applications: EnzAct
(3)
Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #1029734
Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #1029734
Reactivity: Human
Details: Sheep IgG Polyclonal
Reactivity: Human
Details: Sheep IgG Polyclonal
Reactivity: Human
Details: Sheep IgG Polyclonal
Reactivity: Human
Details: Sheep IgG Polyclonal
Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #1029705
Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #1029705
Reactivity: Human
Details: Rabbit IgG Monoclonal Clone #2520B
Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #1029734
Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #1029705
Reactivity: Human
Details: Sheep IgG Polyclonal
Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #1029734
Reactivity: Human
Details: Mouse IgG1 Monoclonal Clone #1029734
Reactivity: Human
Details: Rabbit IgG Monoclonal Clone #2520B

Recombinant Monoclonal Antibody.

Reactivity: Human
Details: Rabbit IgG Monoclonal Clone #2520B
Applications: WB
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