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241 results for "alpha-Galactosidase A/GLA" in Products
alpha-Galactosidase A/GLA Products
Galactosidase alpha encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq]
Reactivity:
Human
Source:
CHO
Accession #:
P06280
Applications:
Enzyme Activity
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF, Simple Western
Reactivity:
Human
Assay Range:
78.13 - 5000 pg/mL
Applications:
ELISA
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
IHC
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
IHC
Reactivity:
Human, Rat
Details:
Rabbit IgG Polyclonal
Applications:
IHC, WB, IP
Reactivity:
Human
Assay Range:
0.78 - 50 ng/mL
Applications:
ELISA
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
WB
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
WB, ICC/IF, IP
Reactivity:
Human
Details:
Mouse IgG1 Monoclonal Clone #1029705
Applications:
IHC
Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #2520B
Applications:
WB
Reactivity:
Human
Details:
Mouse IgG1 Monoclonal Clone #1029734
Applications:
ICC/IF
Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #001
Applications:
ELISA, IP
Reactivity:
E. coli
Source:
E. coli
Accession #:
YP_001464379
Applications:
Enzyme Activity
Reactivity:
Human, Mouse, Rat
Details:
Rabbit IgG Monoclonal Clone #7G8T9
Applications:
WB, ELISA
Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #23GB5545
Applications:
WB, Flow, Mycoplasma
Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #201
Applications:
WB
Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #30H11
Applications:
IHC, ELISA, Flow
Reactivity:
Monkey
Assay Range:
78.13 - 5000 pg/mL
Applications:
ELISA
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF