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241 results for "alpha-Galactosidase A/GLA" in Products

alpha-Galactosidase A/GLA Products

Galactosidase alpha encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq]

Reactivity:
Human
Source:
CHO
Accession #:
P06280
Applications:
Enzyme Activity
(3)
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF, Simple Western
Detection of Human a-Galactosidase A/GLA antibody by Western Blot.
(3)
Reactivity:
Human
Assay Range:
78.13 - 5000 pg/mL
Applications:
ELISA
Human alpha-Galactosidase A/GLA ELISA Kit (Colorimetric)
(2)
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
IHC
Immunohistochemistry-Paraffin: alpha-Galactosidase A/GLA Antibody [NBP1-89796]
(10)
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
IHC
Immunohistochemistry-Paraffin: alpha-Galactosidase A/GLA Antibody [NBP1-89797]
(8)
Reactivity:
Human, Rat
Details:
Rabbit IgG Polyclonal
Applications:
IHC, WB, IP
Immunohistochemistry-Paraffin: alpha-Galactosidase A/GLA Antibody [NBP2-16576]
(4)
Reactivity:
Human
Assay Range:
0.78 - 50 ng/mL
Applications:
ELISA
Human alpha-Galactosidase A/GLA ELISA Kit (Colorimetric)
(2)
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
WB
Western Blot: alpha-Galactosidase A/GLA Antibody [NBP1-58018]
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
WB, ICC/IF, IP
Western Blot: alpha-Galactosidase A/GLA Antibody [H00002717-D01]
(3)
Reactivity:
Human
Details:
Mouse IgG1 Monoclonal Clone #1029705
Applications:
IHC

Recombinant Monoclonal Antibody.

Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #2520B
Applications:
WB
Reactivity:
Human
Details:
Mouse IgG1 Monoclonal Clone #1029734
Applications:
ICC/IF

Recombinant Monoclonal Antibody

Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #001
Applications:
ELISA, IP
Immunoprecipitation: alpha-Galactosidase A/GLA Antibody (001) [NBP2-90047]
Reactivity:
E. coli
Source:
E. coli
Accession #:
YP_001464379
Applications:
Enzyme Activity
R&D Systems Recombinant Proteins and Enzymes

Recombinant Monoclonal Antibody

Reactivity:
Human, Mouse, Rat
Details:
Rabbit IgG Monoclonal Clone #7G8T9
Applications:
WB, ELISA
Western Blot: alpha-Galactosidase A/GLA Antibody (7G8T9) [NBP3-16563]
Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #23GB5545
Applications:
WB, Flow, Mycoplasma
alpha-Galactosidase A/GLA Antibody (23GB5545)
(2)

Recombinant Monoclonal Antibody

Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #201
Applications:
WB
Western Blot: alpha-Galactosidase A/GLA Antibody (201) [NBP2-90048]

Recombinant Monoclonal Antibody

Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #30H11
Applications:
IHC, ELISA, Flow
alpha-Galactosidase A/GLA Antibody (30H11)
(2)
Reactivity:
Monkey
Assay Range:
78.13 - 5000 pg/mL
Applications:
ELISA
Monkey alpha-Galactosidase A/GLA ELISA Kit (Colorimetric)
(2)
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, ICC/IF
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