86 results for "Tripeptidyl-Peptidase I/TPP1" in Products
Tripeptidyl-Peptidase I/TPP1 Products
Tripeptidyl-peptidase I (TPP1), also known as CLN2, is a lysosomal serine protease detected in all tissues examined, with highest levels shown in heart and placenta. It is an aminopeptidase that cleaves tripeptides from the free N-terminus of polypeptides and may also have endopeptidase activity. Defects in TPP1 are the cause of classical late-infantile neuronal ceroid lipofusionosis, also known as ceroid lipofusionosis neuronal 2 (CLN2), a fatal childhood neurodegenerative disease characterized by progressive visual and mental decline, motor disturbance, epilepsy, and behavioral changes.
| Source: | NS0 |
| Accession #: | O14773 |
| Applications: | EnzAct |
| Reactivity: | Human |
| Details: | Mouse IgG1 kappa Monoclonal Clone #3B1 |
| Applications: | IHC, WB, ELISA |
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #254008 |
| Applications: | WB, IP |
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB, IP |
Catalog #:
BAF2237
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB |
Catalog #:
FAB2237N
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #254008 |
| Applications: | WB, IP |
Catalog #:
AF2237G
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB, IP |
Catalog #:
FAB2237U
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #254008 |
| Applications: | WB, IP |
| Reactivity: | Human, Mouse |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC, WB, ICC/IF |
| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC |
| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC |
Catalog #:
FAB2237S
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #254008 |
| Applications: | WB, IP |
Catalog #:
FAB2237X
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #254008 |
| Applications: | WB, IP |
Catalog #:
FAB2237R
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #254008 |
| Applications: | WB, IP |
Catalog #:
AF2237U
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB, IP |
Catalog #:
AF2237V
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB, IP |
Catalog #:
FAB2237V
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #254008 |
| Applications: | WB, IP |
Catalog #:
AF2237R
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB, IP |
Catalog #:
AF2237N
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB, IP |
Catalog #:
AF2237S
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB, IP |
Catalog #:
AF2237T
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB, IP |
Catalog #:
FAB2237T
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #254008 |
| Applications: | WB, IP |
Catalog #:
AF2237X
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |
| Applications: | WB, IP |
Catalog #:
FAB2237G
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #254008 |
| Applications: | WB, IP |
Catalog #:
AF2237AFP594
| Reactivity: | Human |
| Details: | Goat IgG Polyclonal |