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127 results for "beta-Galactosidase-1/GLB1" in Products

beta-Galactosidase-1/GLB1 Products

beta-Galactosidase-1 (GLB1) is a lysosomal beta-galactosidase that hydrolyzes the terminal beta-galactose from ganglioside and keratan sulfate. Defects in this gene are the causes of lysosomal storage diseases for GM1-gangliosidosis and Morquio B syndrome (also known as mucopolysaccharidosis IVB). In GM1 gangliosidosis, GM1 ganglioside accumulates in the neurons of the central nervous system, because of the deficiency (0 plus or minus 3% of normal) of lysosomal beta-galactosidase activity. GM1 ...

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Reactivity:
Human, Canine, Monkey
Details:
Mouse IgG2A Monoclonal Clone #OTI1C9
Applications:
IHC, WB
Western Blot: beta-Galactosidase-1/GLB1 Antibody (OTI1C9) [NBP2-45731]
(16)
Reactivity:
Human, Canine, Monkey
Details:
Mouse IgG2A Monoclonal Clone #OTI1C9
Applications:
IHC, WB
Western Blot: beta-Galactosidase-1/GLB1 Antibody (OTI1C9)Azide and BSA Free [NBP2-70829]
(15)
Reactivity:
Human
Source:
CHO
Accession #:
AAA51819
Applications:
Enzyme Activity
(3)
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, Simple Western
Detection of Human  beta -Galactosidase-1/GLB1 antibody by Western Blot.
(2)
Reactivity:
Human
Details:
Mouse IgG2A Monoclonal Clone #810226
Applications:
WB
Detection of Human  beta -Galactosidase-1/GLB1 antibody by Western Blot.
Reactivity:
Human
Assay Range:
3.13-200 pg/mL
Applications:
ELISA
Human beta-Galactosidase-1/GLB1 ELISA Kit (Colorimetric)
(2)
Reactivity:
Human, Rat
Details:
Rabbit IgG Polyclonal
Applications:
IHC, WB, ICC/IF
Western Blot: beta-Galactosidase-1/GLB1 Antibody [NBP1-32018]
(2)
Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #23GB1580
Applications:
WB, Flow, ICC/IF, Mycoplasma
beta-Galactosidase-1/GLB1 Antibody (23GB1580)
(3)
Reactivity:
Human
Details:
Mouse IgG2a Kappa Monoclonal Clone #6E7
Applications:
WB, ELISA, IP
Western Blot: beta-Galactosidase-1/GLB1 Antibody (6E7) [H00002720-M01]
(4)
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
IHC
Immunohistochemistry-Paraffin: beta-Galactosidase-1/GLB1 Antibody [NBP2-49602]
(3)

Recombinant Monoclonal Antibody

Reactivity:
Human, Mouse, Rat
Details:
Rabbit IgG Monoclonal Clone #S01-3G1
Applications:
WB
Western Blot: beta-Galactosidase-1/GLB1 Antibody (S01-3G1) [NBP3-15007]
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
ICC/IF
beta-Galactosidase-1/GLB1 Antibody - BSA Free Immunocytochemistry/ Immunofluorescence: beta-Galactosidase-1/GLB1 Antibody - BSA Free [NBP2-57793]
Reactivity:
Rat
Assay Range:
0.16 - 10 ng/mL
Applications:
ELISA
Rat beta-Galactosidase-1/GLB1 ELISA Kit (Colorimetric)
(2)
Reactivity:
Mouse, Rat
Details:
Rabbit IgG Polyclonal
Applications:
WB
Western Blot: beta-Galactosidase-1/GLB1 Antibody [NBP3-13394]
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Reactivity:
Human
Details:
Mouse IgG2A Monoclonal Clone #810226
Applications:
WB
Reactivity:
Human
Details:
Mouse IgG2A Monoclonal Clone #810226
Applications:
WB
Reactivity:
Human
Details:
Mouse IgG2A Monoclonal Clone #810226
Applications:
WB
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