125 results for "beta-Galactosidase-1/GLB1" in Products
beta-Galactosidase-1/GLB1 Products
beta-Galactosidase-1 (GLB1) is a lysosomal beta-galactosidase that hydrolyzes the terminal beta-galactose from ganglioside and keratan sulfate. Defects in this gene are the causes of lysosomal storage diseases for GM1-gangliosidosis and Morquio B syndrome (also known as mucopolysaccharidosis IVB). In GM1 gangliosidosis, GM1 ganglioside accumulates in the neurons of the central nervous system, because of the deficiency (0 plus or minus 3% of normal) of lysosomal beta-galactosidase activity. GM1 ...
| Reactivity: | Human, Mouse, Canine, Monkey, Non-species specific |
| Details: | Mouse IgG2A Monoclonal Clone #OTI1C9 |
| Applications: | IHC, WB, ICC/IF |
| Source: | CHO |
| Accession #: | AAA51819 |
| Applications: | EnzAct |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, Simple Western |
| Reactivity: | Human, Canine, Monkey |
| Details: | Mouse IgG2A Monoclonal Clone #OTI1C9 |
| Applications: | IHC, WB |
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #810226 |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Mouse IgG2a Kappa Monoclonal Clone #6E7 |
| Applications: | WB, ELISA, IP |
Catalog #:
FAB6464G
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #810226 |
| Applications: | WB |
Catalog #:
FAB6464V
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #810226 |
| Applications: | WB |
Catalog #:
NBP3-51451
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #23GB1580 |
| Applications: | WB, ICC/IF, Flow, Mycoplasma |
| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC |
Catalog #:
FAB6464S
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #810226 |
| Applications: | WB |
Catalog #:
FAB6464N
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #810226 |
| Applications: | WB |
Catalog #:
FAB6464R
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #810226 |
| Applications: | WB |
Catalog #:
AF6464R
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
Catalog #:
AF6464T
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
Catalog #:
AF6464V
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
Catalog #:
FAB6464T
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #810226 |
| Applications: | WB |
Catalog #:
AF6464N
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
Catalog #:
FAB6464U
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #810226 |
| Applications: | WB |
Catalog #:
FAB6464X
| Reactivity: | Human |
| Details: | Mouse IgG2a Monoclonal Clone #810226 |
| Applications: | WB |
Catalog #:
AF6464X
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
Catalog #:
AF6464U
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
Catalog #:
AF6464G
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
Catalog #:
AF6464S
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
| Reactivity: | Human, Rat |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC, WB, ICC/IF |