92 results for "alpha-L-Iduronidase/IDUA" in Products
alpha-L-Iduronidase/IDUA Products
alpha-L-Iduronidase, encoded by the IDUA gene, is an important enzyme required for the lysosomal degradation of glycosaminoglycans (GAGs). It hydrolyzes the non-reducing terminal a-L-iduronic acid residues in GAGs, including dermatan sulfate and heparan sulfate. Mutations in IDUA that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). MPS I causes progressive cellular, tissue, and organ damage.
NS0-expressed, analyzed by SEC-MALS
| Source: | NS0 |
| Accession #: | AAA81589 |
| Applications: | EnzAct |
Catalog #:
FAB4119AFP594
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
Catalog #:
FAB4119AFP405
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
Catalog #:
AF4119AFP405
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
Catalog #:
AF4119AFP555
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
Catalog #:
FAB4119U
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
| Applications: | WB |
Catalog #:
FAB4119X
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
| Applications: | WB |
Catalog #:
FAB4119AFP555
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
Catalog #:
FAB4119AFP488
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
Catalog #:
AF4119AFP488
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
Catalog #:
FAB4119AFP647
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
Catalog #:
FAB4119AFP680
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
Catalog #:
AF4119AFP594
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
His-tag
| Source: | CHO |
| Accession #: | XP_005554313.1 |
| Applications: | EnzAct |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
Catalog #:
AF4119T
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
Catalog #:
AF4119G
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
Catalog #:
FAB4119V
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
| Applications: | WB |
Catalog #:
AF4119AFP647
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
Catalog #:
AF4119AFP680
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
CHO-expressed (aa 26-653)
| Source: | CHO |
| Accession #: | P35475.2 |
| Applications: | EnzAct |