238 results for "alpha-Galactosidase A/GLA" in Products
alpha-Galactosidase A/GLA Products
Galactosidase alpha encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq]
| Applications: | ELISA |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, Simple Western, ICC |
Catalog #:
FAB6146AFP488
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029705 |
| Source: | CHO |
| Accession #: | P06280 |
| Applications: | EnzAct |
Catalog #:
FAB61461AFP488
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029734 |
Catalog #:
FAB61461AFP680
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029734 |
Catalog #:
AF6146AFP488
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
Catalog #:
AF6146AFP647
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
Catalog #:
AF6146AFP594
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
Catalog #:
AF6146AFP680
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
Catalog #:
FAB6146AFP680
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029705 |
Catalog #:
AF6146X
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, ICC |
Catalog #:
FAB6146AFP594
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029705 |
Catalog #:
FAB61462AFP405
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #2520B |
Catalog #:
FAB61461AFP647
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029734 |
Catalog #:
FAB6146AFP647
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029705 |
Catalog #:
AF6146AFP555
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
Catalog #:
FAB61461AFP405
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029734 |
Catalog #:
FAB61461AFP594
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029734 |
Catalog #:
FAB61462AFP488
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #2520B |
Recombinant Monoclonal Antibody.
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #2520B |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029705 |
| Applications: | IHC |
Catalog #:
AF6146V
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, ICC |
Catalog #:
FAB6146V
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #1029705 |
| Applications: | IHC |
Catalog #:
FAB61462U
Recombinant Monoclonal Antibody.
| Reactivity: | Human |
| Details: | Rabbit IgG Monoclonal Clone #2520B |
| Applications: | WB |