alpha-L-Iduronidase/IDUA Antibody (452619) [PerCP]
Novus Biologicals, part of Bio-Techne | Catalog # FAB4119C
Conjugate
Catalog #
Key Product Details
Species Reactivity
Human
Applications
Western Blot
Label
PerCP (Excitation = 490 nm, Emission = 675 nm)
Antibody Source
Monoclonal Mouse IgG1 Clone # 452619
Concentration
Please see the vial label for concentration. If unlisted please contact technical services.
Product Specifications
Immunogen
Mouse myeloma cell line NS0-derived recombinant human alpha‑L‑Iduronidase/IDUA
Ala26-Pro653 (Ala26Thr)
Accession # P35475.2
Ala26-Pro653 (Ala26Thr)
Accession # P35475.2
Specificity
Detects human alpha‑L‑Iduronidase/IDUA in direct ELISAs and Western blots.
Clonality
Monoclonal
Host
Mouse
Isotype
IgG1
Applications for alpha-L-Iduronidase/IDUA Antibody (452619) [PerCP]
Application
Recommended Usage
Western Blot
Optimal dilutions of this antibody should be experimentally determined.
Application Notes
Optimal dilution of this antibody should be experimentally determined.
Formulation, Preparation, and Storage
Purification
Protein A or G purified from hybridoma culture supernatant
Formulation
PBS
Preservative
0.05% Sodium Azide
Concentration
Please see the vial label for concentration. If unlisted please contact technical services.
Shipping
The product is shipped with polar packs. Upon receipt, store it immediately at the temperature recommended below.
Stability & Storage
Store at 4C in the dark.
Background: alpha-L-Iduronidase/IDUA
alpha-L-Iduronidase, encoded by the IDUA gene, is an important enzyme required for the lysosomal degradation of glycosaminoglycans (GAGs). It hydrolyzes the non-reducing terminal a-L-iduronic acid residues in GAGs, including dermatan sulfate and heparan sulfate. Mutations in IDUA that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). MPS I causes progressive cellular, tissue, and organ damage.
Alternate Names
alphaLIduronidase, IDA, IDUA
Gene Symbol
IDUA
Additional alpha-L-Iduronidase/IDUA Products
Product Documents for alpha-L-Iduronidase/IDUA Antibody (452619) [PerCP]
Product Specific Notices for alpha-L-Iduronidase/IDUA Antibody (452619) [PerCP]
This product is for research use only and is not approved for use in humans or in clinical diagnosis. Primary Antibodies are guaranteed for 1 year from date of receipt.
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