alpha-L-Iduronidase/IDUA Products
alpha-L-Iduronidase, encoded by the IDUA gene, is an important enzyme required for the lysosomal degradation of glycosaminoglycans (GAGs). It hydrolyzes the non-reducing terminal a-L-iduronic acid residues in GAGs, including dermatan sulfate and heparan sulfate. Mutations in IDUA that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). MPS I causes progressive cellular, tissue, and organ damage.
80 results for "alpha-L-Iduronidase/IDUA" in Products
80 results for "alpha-L-Iduronidase/IDUA" in Products
alpha-L-Iduronidase/IDUA Products
alpha-L-Iduronidase, encoded by the IDUA gene, is an important enzyme required for the lysosomal degradation of glycosaminoglycans (GAGs). It hydrolyzes the non-reducing terminal a-L-iduronic acid residues in GAGs, including dermatan sulfate and heparan sulfate. Mutations in IDUA that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). MPS I causes progressive cellular, tissue, and organ damage.
NS0-expressed
| Source: | NS0 |
| Accession #: | AAA81589 |
| Applications: | EnzAct |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
| Applications: | WB |
| Applications: | AC |
His-tag Avi-tag
| Source: | CHO |
| Accession #: | P35475.2 |
| Applications: | BA, EnzAct |
| Source: | NS0 |
| Accession #: | P48441 |
| Applications: | EnzAct |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB |
Fc Chimera
| Source: | CHO |
| Applications: | BA, EnzAct |
His-tag
| Source: | CHO |
| Accession #: | XP_005554313.1 |
| Applications: | EnzAct |
| Reactivity: | Human |
| Details: | Rabbit IgG Polyclonal |
| Applications: | IHC |
CHO-expressed (aa 26-653)
| Source: | CHO |
| Accession #: | P35475.2 |
| Applications: | EnzAct |
CHO-expressed (aa 28-653 H33Q)
| Source: | CHO |
| Accession #: | P35475.2 |
| Applications: | EnzAct |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
| Reactivity: | Human |
| Details: | Sheep IgG Polyclonal |
| Applications: | WB, IP, ICC |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
| Applications: | WB |
| Reactivity: | Human |
| Details: | Mouse IgG1 Monoclonal Clone #452619 |
| Applications: | WB |