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119 results for "beta-Galactosidase-1/GLB1 Antibodies" in Products
beta-Galactosidase-1/GLB1 Antibodies
beta-Galactosidase-1 (GLB1) is a lysosomal beta-galactosidase that hydrolyzes the terminal beta-galactose from ganglioside and keratan sulfate. Defects in this gene are the causes of lysosomal storage diseases for GM1-gangliosidosis and Morquio B syndrome (also known as mucopolysaccharidosis IVB). In GM1 gangliosidosis, GM1 ganglioside accumulates in the neurons of the central nervous system, because of the deficiency (0 plus or minus 3% of normal) of lysosomal beta-galactosidase activity. GM1 ...
Reactivity:
Human, Canine, Monkey
Details:
Mouse IgG2A Monoclonal Clone #OTI1C9
Applications:
IHC, WB
Reactivity:
Human, Canine, Monkey
Details:
Mouse IgG2A Monoclonal Clone #OTI1C9
Applications:
IHC, WB
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB, Simple Western
Reactivity:
Human
Details:
Mouse IgG2A Monoclonal Clone #810226
Applications:
WB
Reactivity:
Human, Rat
Details:
Rabbit IgG Polyclonal
Applications:
IHC, WB, ICC/IF
Reactivity:
Human
Details:
Rabbit IgG Monoclonal Clone #23GB1580
Applications:
WB, Flow, ICC/IF, Mycoplasma
Reactivity:
Human
Details:
Mouse IgG2a Kappa Monoclonal Clone #6E7
Applications:
WB, ELISA, IP
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
IHC
Recombinant Monoclonal Antibody
Reactivity:
Human, Mouse, Rat
Details:
Rabbit IgG Monoclonal Clone #S01-3G1
Applications:
WB
Reactivity:
Human
Details:
Rabbit IgG Polyclonal
Applications:
ICC/IF
Reactivity:
Mouse, Rat
Details:
Rabbit IgG Polyclonal
Applications:
WB
Catalog #:
AF6464G
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Catalog #:
AF6464N
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Catalog #:
AF6464R
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Catalog #:
AF6464S
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Catalog #:
AF6464T
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Catalog #:
AF6464U
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Catalog #:
AF6464V
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Catalog #:
AF6464X
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB
Catalog #:
FAB6464G
Reactivity:
Human
Details:
Mouse IgG2A Monoclonal Clone #810226
Applications:
WB
Catalog #:
FAB6464N
Reactivity:
Human
Details:
Mouse IgG2A Monoclonal Clone #810226
Applications:
WB
Catalog #:
FAB6464N
Reactivity:
Human
Details:
Mouse IgG2A Monoclonal Clone #810226
Applications:
WB
Catalog #:
FAB6464S
Reactivity:
Human
Details:
Mouse IgG2A Monoclonal Clone #810226
Applications:
WB
Catalog #:
FAB6464T
Reactivity:
Human
Details:
Mouse IgG2A Monoclonal Clone #810226
Applications:
WB
Catalog #:
AF6464G
Reactivity:
Human
Details:
Sheep IgG Polyclonal
Applications:
WB